HMSN(CMT) : Recurrent takotsubo cardiomyopathy within a short span of time in a

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Intern Med. 2008;47(18):1609-13.

Recurrent takotsubo cardiomyopathy within a short span of time in a

patient with hereditary motor and sensory neuropathy.

Uechi Y, Higa K.

Department of Internal Medicine, Makiminato Chuou Hospital, Urasoe.

A 53-year-old woman with hereditary motor and sensory neuropathy was

admitted to our hospital with congestive heart failure, followed by

cardiogenic shock and acute renal failure. The patient's neuropathy

was a rare entity documented first in a local area of Okinawa, Japan.

Intensive supportive therapy was performed and the patient recovered

within 4 weeks. Echocardiography revealed takotsubo-type left

ventricular wall motion abnormality at onset. During hospitalization,

restoration and recurrence of apical ballooning were observed at

shorter intervals of days. The unique left ventricular wall motion

abnormality of takotsubo cardiomyopathy is possibly a dynamically

repetitive phenomenon.

Serial echocardiographic studies are necessary so as not to miss

recurrences within short intervals.