An unusual presentation of primary sclerosing cholangitis

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http://www.wjgnet.com/1007-9327/abstract_en.asp?f=6748 & v=14

Goldwire FW, Norris WE, Koff JM, Goodman ZD, MT.An unusual presentation of primary sclerosing cholangitis.World J Gastroenterol 2008 November;14(43):6748-6749An unusual presentation of primary sclerosing cholangitisGoldwire FW, Norris WE, Koff JM, Goodman ZD, MT.Internal Medicine Walter Army Medical Center, Washington DC 20307, United States. franklin.goldwire@...This case report describes the unusual presentation of a patient who had findings which were initially suggestive of a type IV choledochal cyst. Her liver biopsy demonstrated biliary cirrhosis. She was treated with endoscopic retrograde cholangiopancreatography and biliary stent exchanges over one year. Her cholangiogram one year later demonstrated resolution of the biliary cystic dilation which led to her initial diagnosis, with beading and stricturing of the hepatic ducts consistent with primary sclerosing cholangitis. Liver-associated enzymes and physical findings also improved. A liver biopsy one year later demonstrated a marked improvement in hepatic fibrosis with no evidence of cirrhosis.