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Re: RSS and dwarfism

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Jodie I realise you mean well but from everything I have read and been told by

doctors RSS is a type of dwarfism related to Achondroplasia and other forms. The

term 'midget' is deemed offensive and I'm not sure can be applied to RSS people.

You could ask the adults on the site wheteher they consider themselves to be

midgets.

Best wishes

Eileen

Jodi Zwain magicrss@...> wrote:

Jodi R. and others,

While the older literature refers to RSS as a form of dwarfism, it

is not really technically correct. A dwarf is someone who is out of

proportion and looks more like someone with achondroplasia. Our

kids fit the " midget " category, which is short stature and in

proportion. Short stature is under 4'11 " .

HOWEVER, you and your kids will definitely benefit psychologically

if you refer to having RSS as a " growth disorder. " It sounds

better, people don't jump to conclusions and envision one of the

seven dwarfs from Snow White, and it is just plain easier to

comprehend. It is amazing how a little change in wording can make

all the difference in the world.

Meanwhile, speaking of psychological terms and situations, I have

Max home AGAIN because he is vomiting. (Never in my life did I

think that throwing up and vomiting would be such a normal and

regular part of my vocabulary!!!) I truly believe that this is

psychologically based. Each time Max is out of school for more than

a couple of days, he goes through this on the second day back. Dr.

H. prescribed the Transcop patch that is put behind the ear for

motion sickness, so I am trying it out today to see if it helps.

The only problem is that it says it takes 4 hours to be effective.

At least there are no ketones for now. I think I will put him

on " gut rest " and bolus feed him through his g-j button. He HATES

the pump, so this may work. Sigh. There is always something.

Jodi Z.

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I'm afraid I'm going to have to agree with Eileen on this one. RSS is

a form of dwarfism. There are two main types - skeletal dysplasia and

primordial dwarfism. The skeletal dysplasia forms of dwarfism include

achondroplasia. The primordial forms of dwarfism are do not involve

any type of skeletal dysplasia and result in proportionate short

statured individuals. The term midget was coined at the turn of the

17th century in conjuction with P.T. Barnum's exhibition of Tom Thumb,

a proportionate short statured dwarf, who historians and experts now

believe had GHD. The term " midget " is considered to be offensive by

much of the dwarf and greater disability communities because of it's

association with that period of exploitation through display of those

with various short stature causing conditions. In the last ten years

or so, those of us within the dwarf and disability communities have

been trying to distance ourselves from those sorts of conotations. If

anyone is interested in learning more about dwarfism in general, they

can visit Little People of America's website at www.lpaonline.org.

Ther is also a *fantastic* new book out called Little People: The

World Through My Daughter's Eyes by Dan Kennedy (I know you can find

the book on amazon.com, b/c that's where I got it from). He is a

writer who's daughter has a form of dwarfism called achondroplasia.

He does a really good job detailing the history of dwarfism and the

evolution of terminology within both the dwarf and the disability

communities.

~Hillary

21, RSS

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I was told that RSS is a form of dwarfism. It is just a rarer form

that many don't/didn't know existed. It was explained to me that most

people think of dwarfs as having disproportionate limbs to their

bodies, but those with RSS are proportionate, but still considered

dwarfs. Simply because they do have the shortness in stature. But,

yes, you can also say that RSS is a growth disorder. One of my

cousins is an Achondroplasia dwarf.

Just what I have been told,

Jodi R.

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I saw so many email postings on this topic, but having been off the

listserve (I took a break from " MAGIC " for two weeks) I don't have

time to read everything.

Everyone is kind of right.

-Silver Syndrome IS a form a primordial dwarfism. Other

types of primordial do include achrondroplasia. But these are

distinictly different types.

So a child with -Silver syndrome is technically a dwarf.

However, because most general public folks will

immediately " mentally picture " an RSS child as being

achrondroplastic, this causes problems.

Hence, most of us just tell folks that our children have RSS - a

genetic growth disorder that causes them to be shorter in stature

and to have difficulty gaining weight, often with a lot of

intestinal issues.

The problem is that achrondr. have skeletal dysplasia, and therefore

can NOT use growth hormone, without serious risk to their health.

RSS children do NOT have skeletal dysplasia; they may have limb

asymmetry but this is NOT skeletal dysplasia.

I hope that this helps clarify things.

Salem

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--...the origional post stated that RSS children were not

dwarves but infact midgets! I really don't want to open this whole

can of worms again but that was the initial gist which I took great

umbrage at!!Eileen - In RSS-Support , " magicrss "

wrote:

> I saw so many email postings on this topic, but having been off

the

> listserve (I took a break from " MAGIC " for two weeks) I don't have

> time to read everything.

>

> Everyone is kind of right.

>

> -Silver Syndrome IS a form a primordial dwarfism. Other

> types of primordial do include achrondroplasia. But these are

> distinictly different types.

>

> So a child with -Silver syndrome is technically a dwarf.

> However, because most general public folks will

> immediately " mentally picture " an RSS child as being

> achrondroplastic, this causes problems.

>

> Hence, most of us just tell folks that our children have RSS - a

> genetic growth disorder that causes them to be shorter in stature

> and to have difficulty gaining weight, often with a lot of

> intestinal issues.

>

> The problem is that achrondr. have skeletal dysplasia, and

therefore

> can NOT use growth hormone, without serious risk to their health.

> RSS children do NOT have skeletal dysplasia; they may have limb

> asymmetry but this is NOT skeletal dysplasia.

>

> I hope that this helps clarify things.

>

> Salem

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